MR Vol.14 No.3 indexに戻る

MODERN RHEUMATOLOGY Vol.14 No.3             
A case of pneumatosis cystoides intestinalis in a patient with polymyositis and interstitial pneumonia
Yoko Wada1, 2 , Naoya Murayama1, Shintaro Hirose1, Hian In1, Takeshi Kuroda2, Satoshi Ito2, Masaaki Nakano3 and Fumitake Gejyo2
(1) Department of Internal Medicine, Nagaoka Central General Hospital, Nagaoka, Japan
(2) Division of Clinical Nephrology and Rheumatology, Niigata University Graduate School of Medical and Dental Sciences, 1-757, Asahimachi-dori, Niigara, 951-8510, Japan
(3) School of Health Sciences, Faculty of Medicine, Niigata University, Niigata, Japan
Received: 18 September 2003 Accepted: 03 March 2004
Abstract
 We report the case of a 49-year-old man who presented with pneumatosis cystoides intestinalis associated with polymyositis and interstitial pneumonia. Three months after the administration of prednisolone and cyclosporine, he noticed mild abdominal distension, and a radiographic examination showed intraperitoneal free gas and intramural gas, suggestive of pneumatosis cystoides intestinalis (PCI). Additional treatment with a combination of doxycycline and high-dose oxygen therapy was effective in relieving the clinical symptoms and reducing the intramural gas.
 
Key words
Intersitial pneumonia - Pneumatosis cystoides intestinalis (PCI) - Polymyositis
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