Three cases of pneumatosis intestinalis presenting in autoimmune diseases
Akihiro Sagara1,2 , Kiyoki Kitagawa2 , Kengo Furuichi2 , Shinji Kitajima2 , Tadashi Toyama2 , Toshiya Okumura1,2 , Akinori Hara2 , Yoshio Sakai3 , Shuichi Kaneko2 , Takashi Wada3
15 June 2011
18 October 2011
9 November 2011
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Pneumatosis intestinalis (PI) is a comparatively rare disease characterized by the presence of intramural gas in the gastrointestinal tract. PI is known to be associated with several clinical conditions, such as pulmonary diseases, gastrointestinal diseases, and traumatic injury, as well as autoimmune disorders. In particular, PI is commonly seen in systemic sclerosis (SSc) but rarely in systemic lupus erythematosus and dermatomyositis (DM). In this report, we present three cases of PI presenting in autoimmune diseases, including DM, Sjögren’s syndrome, and limited SSc, and further discuss its background characteristics.
Pneumatosis intestinalis - Autoimmune diseases