Vol.22 No.4

Case Report

Three cases of pneumatosis intestinalis presenting in autoimmune diseases

Authors

Akihiro Sagara1,2 , Kiyoki Kitagawa2 , Kengo Furuichi2 , Shinji Kitajima2 , Tadashi Toyama2 , Toshiya Okumura1,2 , Akinori Hara2 , Yoshio Sakai3 , Shuichi Kaneko2 , Takashi Wada3

  • Department of Nephrology and Hypertension, Tonami General Hospital, 1-61, Sintomicho, Tonami, 939-1395, Japan
  • Department of Disease Control and Homeostasis, Institute of Medical, Pharmaceutical and Health Sciences, Faculty of Medicine, Kanazawa University, 13-1 Takara-machi, Kanazawa, 920-8641, Japan
  • Department of Laboratory Medicine, Institute of Medical, Pharmaceutical and Health Sciences, Faculty of Medicine, Kanazawa University, 13-1 Takara-machi, Kanazawa, 920-8641, Japan
Received:

15 June 2011

Accepted:

18 October 2011

Published online:

9 November 2011

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Abstract

Pneumatosis intestinalis (PI) is a comparatively rare disease characterized by the presence of intramural gas in the gastrointestinal tract. PI is known to be associated with several clinical conditions, such as pulmonary diseases, gastrointestinal diseases, and traumatic injury, as well as autoimmune disorders. In particular, PI is commonly seen in systemic sclerosis (SSc) but rarely in systemic lupus erythematosus and dermatomyositis (DM). In this report, we present three cases of PI presenting in autoimmune diseases, including DM, Sjögren’s syndrome, and limited SSc, and further discuss its background characteristics.

Key words

Pneumatosis intestinalis - Autoimmune diseases