Vol.22 No.3

Case Report

Nephrocalcinosis: a rare presenting manifestation of primary Sjögren’s syndrome

Authors

Rajesh Rajput1,2,3 , Ashish Sehgal3 , Deepak Jain3 , Rajeev Sen4 , Ompal Saini3

  • Department of Endocrinology and Medicine Unit VII, Pt. B.D. Sharma Post Graduate Institute of Medical Sciences, Rohtak, 124001, Haryana, India
  • 241, Sector 2, Rohtak, 124001, Haryana, India
  • Department of Medicine, Pt. B.D. Sharma Post Graduate Institute of Medical Sciences, Rohtak, 124001, Haryana, India
  • Department of Pathology, Pt. B.D. Sharma Post Graduate Institute of Medical Sciences, Rohtak, 124001, Haryana, India
Received:

15 July 2011

Accepted:

21 September 2011

Published online:

9 October 2011

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Abstract

Renal involvement in primary Sjögren’s syndrome (pSS) is not uncommon. Autoimmune tubulointerstitial disorders and distal renal tubular acidosis (dRTA) account for majority of the cases of renal involvement. While dRTA may precede the onset of sicca syndrome in pSS, nephrocalcinosis as a presenting manifestation of pSS is rare. Here, to emphasize the need for initiating investigations for pSS in any patient presenting with nephrocalcinosis due to dRTA, we report a 21-year-old woman presenting with nephrocalcinosis long before pSS was objectively diagnosed.

Key words

Distal renal tubular acidosis (dRTA) - Primary Sjögren’s syndrome (pSS) - Nephrocalcinosis