Takayasu disease with prominent pulmonary artery involvement: confusion with pulmonary disease leading to delayed diagnosis
Bilgehan Karadag1 , Hasan Kilic2 , Dursun Duman1 , Zeki Ongen1 , Vural Ali Vural1 , Hasan Yazici2
12 March 2008
14 April 2008
27 May 2008
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Pulmonary artery involvement as the initial predominant clinical manifestation in Takayasu arteritis (TA) is rare. We describe a young adult female who presented with life-threatening complications of proximal pulmonary arterial involvement of Takayasu arteritis. In our case, atypical presentation of TA with pulmonary symptoms due to pulmonary artery involvement resulted in an erroneous initial diagnosis of sarcoidosis and then tuberculosis. The frequency of such a clinical form could be underestimated given the difficulties involved in its diagnosis and because its features are similar to those of pulmonary disease.
Takayasu arteritis - Pulmonary artery involvement