CASE REPORT
Asynchronous progressive diaphyseal dysplasia
Toshinori Sakai1, Yoshito Matsui1, Shinsuke Katoh1, Kiminori Yukata1, Daisuke Hamada1, Yoichiro Takata1, Hiromichi Yokoi2 and Natsuo Yasui1
| (1) |
Department of Orthopedics, Institute of Health Biosciences, The University of Tokushima Graduate School, 3-18-15 Kuramoto-cho, Tokushima 770-8503, Japan |
| (2) |
Department of Orthopedics, National Kagawa Children's Hospital, Kagawa, Japan |
Received: 21 June 2005 Accepted: 13 October 2005
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Abstract We report the case of a 42-year-old Japanese woman with unusual diaphyseal dysplasia of bilateral femora. Radiographs showed thickening and sclerosis of the cortex with resultant enlargement of the diaphysis, unclear demarcation of the surface of the cortex, and no periosteal reaction. These changes were found on the left femur at the first presentation, and those on the right femur developed within several years. Although this patient partly presented characteristics of Ribbing disease and Camurati Engelmann disease, the focal involvement of bilateral femora suggested an unknown pathogenesis.
Key words Asynchronous onset - Caffey disease - Camurati Engelmann disease - Diaphyseal dysplasia - Femur - Ribbing disease |
