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MODERN RHEUMATOLOGY Vol.14 No.3
>MR14-3
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| A case of pneumatosis cystoides intestinalis in a patient with polymyositis and interstitial pneumonia |
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| Yoko Wada1, 2 , Naoya Murayama1, Shintaro Hirose1, Hian In1, Takeshi Kuroda2, Satoshi Ito2, Masaaki Nakano3 and Fumitake Gejyo2 |
(1) Department of Internal Medicine, Nagaoka Central General Hospital, Nagaoka, Japan
(2) Division of Clinical Nephrology and Rheumatology, Niigata University Graduate School of Medical and Dental Sciences, 1-757, Asahimachi-dori, Niigara, 951-8510, Japan
(3) School of Health Sciences, Faculty of Medicine, Niigata University, Niigata, Japan |
Received: 18 September 2003 Accepted: 03 March 2004 |
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Abstract |
| We report the case of a 49-year-old man who presented with pneumatosis cystoides intestinalis associated with polymyositis and interstitial pneumonia. Three months after the administration of prednisolone and cyclosporine, he noticed mild abdominal distension, and a radiographic examination showed intraperitoneal free gas and intramural gas, suggestive of pneumatosis cystoides intestinalis (PCI). Additional treatment with a combination of doxycycline and high-dose oxygen therapy was effective in relieving the clinical symptoms and reducing the intramural gas. |
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| Key words |
| Intersitial pneumonia - Pneumatosis cystoides intestinalis (PCI) - Polymyositis |
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